Mohammad Taghi Chitsazi
1,2, Adileh Shirmohammadi
1,2*, Nasrin Rahmanpour
3, Monir Moradzadeh Khiyavi
41 Dental and Periodontal Research Center, Tabriz University of Medical Sciences, Tabriz, Iran
2 Associate Professor, Department of Peiodontics, Faculty of Dentistry, Tabriz University of Medical Sciences, Tabriz, Iran
3 Postgraduate Student, Department of Prosthothdontics, Faculty of Dentistry, Tabriz University of Medical Sciences, Tabriz, Iran
4 Associate Professor, Departments of Oral Pathology, Faculty of Dentistry, Tehran University of Medical Sciences, International Campus, Tehran, Iran
Abstract
The Sturge-Weber syndrome or encephalotrigeminal angiomatosis is a rare neurological and congenital disorder with a
frequency of 1 in 50,000 births. This syndrome is a nonhereditary developmental condition and is characterized by the
presence of congenital capillary malformation and a hamartomatous vascular proliferation involving the face (port-wine
stain or facial birthmark), sometimes skull and the tissues of brain, jaws, oral soft and hard tissues and rarely other body
organs. Seizures, mental retardation, and cortical calcification (tram-tracks) and congenital glaucoma may be seen in this
syndrome. We report here a 40-year-old female with Sturge-Weber syndrome associated with bilateral cutaneous capillary
malformation on her face, neck, hands and feet and also gingival enlargement.